Anti-CPS1 Polyclonal Antibody-一抗-抗体-蛋白与免疫

Anti-CPS1 Polyclonal Antibody

品牌:solarbio | 货号:K007950P

英文名称 Anti-CPS1 Polyclonal Antibody
宿主 Rabbit
别名 PHN;CPSASE1
应用 IHC
稀释比例 IHC 1:30-150.
交叉反应 Human Mouse Rat
蛋白分子量 165/116kDa
Gene ID 1373
保存 Store at -20°C. Avoid freeze / thaw cycles.
储存液 Buffer: PBS with 0.03% Proclin300, 50% glycerol, pH7.3.
纯化方法 Affinity purification
亚型 IgG
免疫原 A synthetic peptide of human CPS1
性状 液体
Public Immunogen Range A synthetic peptide of human CPS1
Subcellular Locations Cytoplasm Nucleus
Swiss Prot P31327
克隆类型 Polyclonal Antibody
背景资料 The mitochondrial enzyme encoded by this gene catalyzes synthesis of carbamoyl phosphate from ammonia and bicarbonate. This reaction is the first committed step of the urea cycle, which is important in the removal of excess urea from cells. The encoded protein may also represent a core mitochondrial nucleoid protein. Three transcript variants encoding different isoforms have been found for this gene. The shortest isoform may not be localized to the mitochondrion. Mutations in this gene have been associated with carbamoyl phosphate synthetase deficiency, susceptibility to persistent pulmonary hypertension, and susceptibility to venoocclusive disease after bone marrow transplantation.