Anti-CPS1 Polyclonal Antibody
品牌：solarbio | 货号：K007950P
| 英文名称 | Anti-CPS1 Polyclonal Antibody |
|---|---|
| 宿主 | Rabbit |
| 别名 | PHN;CPSASE1 |
| 应用 | IHC |
| 稀释比例 | IHC 1:30-150. |
| 交叉反应 | Human Mouse Rat |
| 蛋白分子量 | 165/116kDa |
| Gene ID | 1373 |
| 保存 | Store at -20°C. Avoid freeze / thaw cycles. |
| 储存液 | Buffer: PBS with 0.03% Proclin300, 50% glycerol, pH7.3. |
| 纯化方法 | Affinity purification |
| 亚型 | IgG |
| 免疫原 | A synthetic peptide of human CPS1 |
| 性状 | 液体 |
| Public Immunogen Range | A synthetic peptide of human CPS1 |
| Subcellular Locations | Cytoplasm Nucleus |
| Swiss Prot | P31327 |
| 克隆类型 | Polyclonal Antibody |
| 背景资料 | The mitochondrial enzyme encoded by this gene catalyzes synthesis of carbamoyl phosphate from ammonia and bicarbonate. This reaction is the first committed step of the urea cycle, which is important in the removal of excess urea from cells. The encoded protein may also represent a core mitochondrial nucleoid protein. Three transcript variants encoding different isoforms have been found for this gene. The shortest isoform may not be localized to the mitochondrion. Mutations in this gene have been associated with carbamoyl phosphate synthetase deficiency, susceptibility to persistent pulmonary hypertension, and susceptibility to venoocclusive disease after bone marrow transplantation. |