Anti-FH Polyclonal Antibody
品牌：solarbio | 货号：K004139P
| 英文名称 | Anti-FH Polyclonal Antibody |
|---|---|
| 宿主 | Rabbit |
| 别名 | FMRD;HLRCC;LRCC;MCL;MCUL1 |
| 应用 | WB IF |
| 稀释比例 | WB 1:500-2000. IF 1:10-100. |
| 交叉反应 | Human Mouse Rat |
| 蛋白分子量 | 55kDa |
| Gene ID | 2271 |
| 保存 | Store at -20°C. Avoid freeze / thaw cycles. |
| 储存液 | Buffer: PBS with 0.02% sodium azide, 50% glycerol, pH7.3. |
| 纯化方法 | Affinity purification |
| 亚型 | IgG |
| 免疫原 | Recombinant protein of human FH |
| 性状 | 液体 |
| Public Immunogen Range | Recombinant protein of human FH |
| Subcellular Locations | Cytoplasm Mitochondrion |
| Swiss Prot | P07954 |
| 克隆类型 | Polyclonal Antibody |
| 背景资料 | The protein encoded by this gene is an enzymatic component of the tricarboxylic acid (TCA) cycle, or Krebs cycle, and catalyzes the formation of L-malate from fumarate. It exists in both a cytosolic form and an N-terminal extended form, differing only in the translation start site used. The N-terminal extended form is targeted to the mitochondrion, where the removal of the extension generates the same form as in the cytoplasm. It is similar to some thermostable class II fumarases and functions as a homotetramer. Mutations in this gene can cause fumarase deficiency and lead to progressive encephalopathy. |