Anti-GALNS Polyclonal Antibody-一抗-抗体-蛋白与免疫

Anti-GALNS Polyclonal Antibody

品牌:solarbio | 货号:K004010P

英文名称 Anti-GALNS Polyclonal Antibody
宿主 Rabbit
别名 GALNAC6S;GAS;GalN6S;MPS4A
应用 WB IHC
稀释比例 WB 1:500-2000. IHC 1:50-200.
交叉反应 Human Mouse
蛋白分子量 58kDa
Gene ID 2588
保存 Store at -20°C. Avoid freeze / thaw cycles.
储存液 Buffer: PBS with 0.02% sodium azide, 50% glycerol, pH7.3.
纯化方法 Affinity purification
亚型 IgG
免疫原 Recombinant protein of human GALNS
性状 液体
Public Immunogen Range Recombinant protein of human GALNS
Subcellular Locations Lysosome
Swiss Prot P34059
克隆类型 Polyclonal Antibody
背景资料 This gene encodes N-acetylgalactosamine-6-sulfatase which is a lysosomal exohydrolase required for the degradation of the glycosaminoglycans, keratan sulfate, and chondroitin 6-sulfate. Sequence alterations including point, missense and nonsense mutations, as well as those that affect splicing, result in a deficiency of this enzyme. Deficiencies of this enzyme lead to Morquio A syndrome, a lysosomal storage disorder.