Anti-GALNS Polyclonal Antibody
品牌:solarbio | 货号:K004010P
| 英文名称 | Anti-GALNS Polyclonal Antibody |
|---|---|
| 宿主 | Rabbit |
| 别名 | GALNAC6S;GAS;GalN6S;MPS4A |
| 应用 | WB IHC |
| 稀释比例 | WB 1:500-2000. IHC 1:50-200. |
| 交叉反应 | Human Mouse |
| 蛋白分子量 | 58kDa |
| Gene ID | 2588 |
| 保存 | Store at -20°C. Avoid freeze / thaw cycles. |
| 储存液 | Buffer: PBS with 0.02% sodium azide, 50% glycerol, pH7.3. |
| 纯化方法 | Affinity purification |
| 亚型 | IgG |
| 免疫原 | Recombinant protein of human GALNS |
| 性状 | 液体 |
| Public Immunogen Range | Recombinant protein of human GALNS |
| Subcellular Locations | Lysosome |
| Swiss Prot | P34059 |
| 克隆类型 | Polyclonal Antibody |
| 背景资料 | This gene encodes N-acetylgalactosamine-6-sulfatase which is a lysosomal exohydrolase required for the degradation of the glycosaminoglycans, keratan sulfate, and chondroitin 6-sulfate. Sequence alterations including point, missense and nonsense mutations, as well as those that affect splicing, result in a deficiency of this enzyme. Deficiencies of this enzyme lead to Morquio A syndrome, a lysosomal storage disorder. |