Anti-HADHA Polyclonal Antibody
品牌：solarbio | 货号：K106876P
| 英文名称 | Anti-HADHA Polyclonal Antibody |
|---|---|
| 宿主 | Rabbit |
| 别名 | ECHA;GBP;HADH;LCEH;LCHAD;MTPA;TP-ALPHA;trifunctional enzyme subunit alpha;mitochondrial |
| 应用 | IHC |
| 稀释比例 | IHC 1:50-200. |
| 交叉反应 | Human |
| 蛋白分子量 | 83kDa |
| Gene ID | 3030 |
| 保存 | Store at -20°C. Avoid freeze / thaw cycles. |
| 储存液 | Buffer: PBS with 0.03% Proclin300, 50% glycerol, pH7.3. |
| 纯化方法 | Affinity purification |
| 亚型 | IgG |
| 免疫原 | A synthetic peptide of human HADHA |
| 性状 | 液体 |
| Public Immunogen Range | A synthetic peptide of human HADHA |
| Subcellular Locations | Cytoplasm |
| Swiss Prot | P40939 |
| 克隆类型 | Polyclonal Antibody |
| 背景资料 | This gene encodes the alpha subunit of the mitochondrial trifunctional protein, which catalyzes the last three steps of mitochondrial beta-oxidation of long chain fatty acids. The mitochondrial membrane-bound heterocomplex is composed of four alpha and four beta subunits, with the alpha subunit catalyzing the 3-hydroxyacyl-CoA dehydrogenase and enoyl-CoA hydratase activities. Mutations in this gene result in trifunctional protein deficiency or LCHAD deficiency. The genes of the alpha and beta subunits of the mitochondrial trifunctional protein are located adjacent to each other in the human genome in a head-to-head orientation. |