Anti-ETFA Polyclonal Antibody
品牌:solarbio | 货号:K005383P
英文名称 |
Anti-ETFA Polyclonal Antibody |
宿主 |
Rabbit |
别名 |
EMA;GA2;MADD |
应用 |
WB IHC IF |
稀释比例 |
WB 1:500-2000. IHC 1:50-200. IF 1:50-100. |
交叉反应 |
Human Mouse Rat |
蛋白分子量 |
35kDa |
Gene ID |
2108 |
保存 |
Store at -20°C. Avoid freeze / thaw cycles. |
储存液 |
Buffer: PBS with 0.02% sodium azide, 50% glycerol, pH7.3. |
纯化方法 |
Affinity purification |
亚型 |
IgG |
免疫原 |
Recombinant protein of human ETFA |
性状 |
液体 |
Public Immunogen Range |
Recombinant protein of human ETFA |
Subcellular Locations |
Mitochondrion matrix |
Swiss Prot |
P13804 |
克隆类型 |
Polyclonal Antibody |
背景资料 |
ETFA participates in catalyzing the initial step of the mitochondrial fatty acid beta-oxidation. It shuttles electrons between primary flavoprotein dehydrogenases and the membrane-bound electron transfer flavoprotein ubiquinone oxidoreductase. Defects in electron-transfer-flavoprotein have been implicated in type II glutaricaciduria in which multiple acyl-CoA dehydrogenase deficiencies result in large excretion of glutaric, lactic, ethylmalonic, butyric, isobutyric, 2-methyl-butyric, and isovaleric acids. Two transcript variants encoding different isoforms have been found for this gene. |