Anti-GNS Polyclonal Antibody
品牌：solarbio | 货号：K005286P
| 英文名称 | Anti-GNS Polyclonal Antibody |
|---|---|
| 宿主 | Rabbit |
| 别名 | G6S |
| 应用 | WB |
| 稀释比例 | WB 1:500-2000. |
| 交叉反应 | Human Mouse Rat |
| 蛋白分子量 | 62kDa |
| Gene ID | 2799 |
| 保存 | Store at -20°C. Avoid freeze / thaw cycles. |
| 储存液 | Buffer: PBS with 0.02% sodium azide, 50% glycerol, pH7.3. |
| 纯化方法 | Affinity purification |
| 亚型 | IgG |
| 免疫原 | Recombinant protein of human GNS |
| 性状 | 液体 |
| Public Immunogen Range | Recombinant protein of human GNS |
| Subcellular Locations | Lysosome |
| Swiss Prot | P15586 |
| 克隆类型 | Polyclonal Antibody |
| 背景资料 | The product of this gene is a lysosomal enzyme found in all cells. It is involved in the catabolism of heparin, heparan sulphate, and keratan sulphate. Deficiency of this enzyme results in the accumulation of undegraded substrate and the lysosomal storage disorder mucopolysaccharidosis type IIID (Sanfilippo D syndrome). Mucopolysaccharidosis type IIID is the least common of the four subtypes of Sanfilippo syndrome. |