Anti-SGSH Polyclonal Antibody-一抗-抗体-蛋白与免疫

Anti-SGSH Polyclonal Antibody

品牌:solarbio | 货号:K005682P

英文名称 Anti-SGSH Polyclonal Antibody
宿主 Rabbit
别名 HSS;MPS3A;SFMD
应用 WB IHC
稀释比例 WB 1:500-2000. IHC 1:50-100.
交叉反应 Human Mouse Rat
蛋白分子量 57kDa
Gene ID 6448
保存 Store at -20°C. Avoid freeze / thaw cycles.
储存液 Buffer: PBS with 0.02% sodium azide, 50% glycerol, pH7.3.
纯化方法 Affinity purification
亚型 IgG
免疫原 Recombinant protein of human SGSH
性状 液体
Public Immunogen Range Recombinant protein of human SGSH
Subcellular Locations Lysosome
Swiss Prot P51688
克隆类型 Polyclonal Antibody
背景资料 This gene encodes one of several enzymes involved in the lysosomal degradation of heparan sulfate. Mutations in this gene are associated with Sanfilippo syndrome A, one type of the lysosomal storage disease mucopolysaccaridosis III, which results from impaired degradation of heparan sulfate. Transcripts of varying sizes have been reported but their biological validity has not been determined.