Anti-SGSH Polyclonal Antibody
品牌:solarbio | 货号:K005682P
英文名称 |
Anti-SGSH Polyclonal Antibody |
宿主 |
Rabbit |
别名 |
HSS;MPS3A;SFMD |
应用 |
WB IHC |
稀释比例 |
WB 1:500-2000. IHC 1:50-100. |
交叉反应 |
Human Mouse Rat |
蛋白分子量 |
57kDa |
Gene ID |
6448 |
保存 |
Store at -20°C. Avoid freeze / thaw cycles. |
储存液 |
Buffer: PBS with 0.02% sodium azide, 50% glycerol, pH7.3. |
纯化方法 |
Affinity purification |
亚型 |
IgG |
免疫原 |
Recombinant protein of human SGSH |
性状 |
液体 |
Public Immunogen Range |
Recombinant protein of human SGSH |
Subcellular Locations |
Lysosome |
Swiss Prot |
P51688 |
克隆类型 |
Polyclonal Antibody |
背景资料 |
This gene encodes one of several enzymes involved in the lysosomal degradation of heparan sulfate. Mutations in this gene are associated with Sanfilippo syndrome A, one type of the lysosomal storage disease mucopolysaccaridosis III, which results from impaired degradation of heparan sulfate. Transcripts of varying sizes have been reported but their biological validity has not been determined. |