Anti-OTC Polyclonal Antibody
品牌:solarbio | 货号:K006077P
英文名称 |
Anti-OTC Polyclonal Antibody |
宿主 |
Rabbit |
别名 |
OCTD |
应用 |
WB IHC |
稀释比例 |
WB 1:1000-4000. IHC 1:50-100. |
交叉反应 |
Human Mouse Rat |
蛋白分子量 |
40kDa |
Gene ID |
5009 |
保存 |
Store at -20°C. Avoid freeze / thaw cycles. |
储存液 |
Buffer: PBS with 0.02% sodium azide, 50% glycerol, pH7.3. |
纯化方法 |
Affinity purification |
亚型 |
IgG |
免疫原 |
Recombinant protein of human OTC |
性状 |
液体 |
Public Immunogen Range |
Recombinant protein of human OTC |
Subcellular Locations |
Mitochondrion matrix |
Swiss Prot |
P00480 |
克隆类型 |
Polyclonal Antibody |
背景资料 |
This nuclear gene encodes a mitochondrial matrix enzyme. Missense, nonsense, and frameshift mutations in this enzyme lead to ornithine transcarbamylase deficiency, which causes hyperammonemia. Since the gene for this enzyme maps close to that for Duchenne muscular dystrophy, it may play a role in that disease also. |