Anti-OTC Polyclonal Antibody-一抗-抗体-蛋白与免疫

Anti-OTC Polyclonal Antibody

品牌:solarbio | 货号:K006077P

英文名称 Anti-OTC Polyclonal Antibody
宿主 Rabbit
别名 OCTD
应用 WB IHC
稀释比例 WB 1:1000-4000. IHC 1:50-100.
交叉反应 Human Mouse Rat
蛋白分子量 40kDa
Gene ID 5009
保存 Store at -20°C. Avoid freeze / thaw cycles.
储存液 Buffer: PBS with 0.02% sodium azide, 50% glycerol, pH7.3.
纯化方法 Affinity purification
亚型 IgG
免疫原 Recombinant protein of human OTC
性状 液体
Public Immunogen Range Recombinant protein of human OTC
Subcellular Locations Mitochondrion matrix
Swiss Prot P00480
克隆类型 Polyclonal Antibody
背景资料 This nuclear gene encodes a mitochondrial matrix enzyme. Missense, nonsense, and frameshift mutations in this enzyme lead to ornithine transcarbamylase deficiency, which causes hyperammonemia. Since the gene for this enzyme maps close to that for Duchenne muscular dystrophy, it may play a role in that disease also.