Anti-GATM Polyclonal Antibody-一抗-抗体-蛋白与免疫

Anti-GATM Polyclonal Antibody

品牌:solarbio | 货号:K004646P

英文名称 Anti-GATM Polyclonal Antibody
宿主 Rabbit
别名 AGAT;AT;CCDS3
应用 WB IHC IF
稀释比例 WB 1:500-2000. IHC 1:50-200. IF 1:50-200.
交叉反应 Human Mouse Rat
蛋白分子量 48kDa
Gene ID 2628
保存 Store at -20°C. Avoid freeze / thaw cycles.
储存液 Buffer: PBS with 0.02% sodium azide, 50% glycerol, pH7.3.
纯化方法 Affinity purification
亚型 IgG
免疫原 Recombinant protein of human GATM
性状 液体
Public Immunogen Range Recombinant protein of human GATM
Subcellular Locations Cytoplasm Intermembrane side Mitochondrion inner membrane Peripheral membrane protein
Swiss Prot P50440
克隆类型 Polyclonal Antibody
背景资料 This gene encodes a mitochondrial enzyme that belongs to the amidinotransferase family. This enzyme is involved in creatine biosynthesis, whereby it catalyzes the transfer of a guanido group from L-arginine to glycine, resulting in guanidinoacetic acid, the immediate precursor of creatine. Mutations in this gene cause arginine:glycine amidinotransferase deficiency, an inborn error of creatine synthesis characterized by mental retardation, language impairment, and behavioral disorders.