Anti-PCCA Polyclonal Antibody
品牌:solarbio | 货号:K006034P
英文名称 |
Anti-PCCA Polyclonal Antibody |
宿主 |
Rabbit |
别名 |
PCCA |
应用 |
WB |
稀释比例 |
WB 1:1000-3000. |
交叉反应 |
Human Mouse Rat |
蛋白分子量 |
80kDa |
Gene ID |
5095 |
保存 |
Store at -20°C. Avoid freeze / thaw cycles. |
储存液 |
Buffer: PBS with 0.02% sodium azide, 50% glycerol, pH7.3. |
纯化方法 |
Affinity purification |
亚型 |
IgG |
免疫原 |
Recombinant protein of human PCCA |
性状 |
液体 |
Public Immunogen Range |
Recombinant protein of human PCCA |
Subcellular Locations |
Mitochondrion matrix |
Swiss Prot |
P05165 |
克隆类型 |
Polyclonal Antibody |
背景资料 |
The protein encoded by this gene is the alpha subunit of the heterodimeric mitochondrial enzyme Propionyl-CoA carboxylase. PCCA encodes the biotin-binding region of this enzyme. Mutations in either PCCA or PCCB (encoding the beta subunit) lead to an enzyme deficiency resulting in propionic acidemia. Multiple transcript variants encoding different isoforms have been found for this gene. |